Regular articleCongenital simple hamartoma of the retinal pigment epithelium: A study of five cases☆
Section snippets
Case reports
A summary of the clinical, fluorescein angiographic, and ultrasonographic features of these five cases is provided in Table 1, Table 2.
Discussion
Congenital hamartoma of the RPE was described by Laqua5 in 1981, based on clinical observations in two cases. He reported a 39-year-old man with decreased vision from a jet-black parafoveal tumor of 1 mm basal dimension that projected through full-thickness retina into the vitreous cavity. Minimally dilated feeding vessels were noted. This lesion remained stable for 15 years. The second case was a 15-year-old boy with good visual acuity and a 0.5-mm black, full-thickness retinal tumor,
Acknowledgements
The authors thank Dr. Richard Chenowith, Dr. Cathy Colt, and Dr. Bruce Schnall, each for referral of a patient included in this series.
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Manuscript no. 220306
Supported by the Eye Tumor Research Foundation, Philadelphia, Pennsylvania (CLS); the Macula Foundation, New York, New York (CLS); the Rosenthal Award of the Macula Society Barcelona, Spain (CLS); and the Paul Kayser International Award of Merit in Retina Research, Houston, Texas (JAS).