Case ReportBenign fibrous histiocytoma of the ethmoids in an infant
Introduction
Benign fibrous histiocytoma (BFH) is a benign neoplasm of mesenchymal origin composed of histiocytes and fibroblasts.1 It is commonly found as the cutaneous form in the sun exposed skin and rarely as a non-cutaneous lesion in the head and neck. We report the clinical and pathological aspects of a rare case of BFH of the ethmoid sinus in a nine-month-old male infant patient treated at our center.
Section snippets
Case report
A nine-month-old male infant patient was referred to our center with history of nasal blockage left side and protrusion of left eyeball of 2 months duration. The parents gave history of insidious onset, painless, progressive protrusion of the left eyeball of their son. The patient was a full term normal delivery of a non-consanguineous marriage with normal milestones. There was no history of nasal discharge, epistaxis or birth trauma. On clinical evaluation the patient had proptosis of left eye
Discussion
Fibrous histiocytic tumors comprise a group of lesions with certain overlapping morphologic features but with variable origin and biologic behavior. Fibrous histiocytoma, a soft tissue tumor also referred to as fibrous xanthoma, dermatofibroma, xanthogranuloma and fibroxanthoma was first described as a separate clinical entity in the 1960.2, 3 BFH is a common benign neoplasm found in the sun exposed dermis and superficial subcutaneous tissue of the extremities, but is also found less frequently
Conclusion
Benign fibrous histiocytoma is a rare benign tumor with characteristic histopathological features, which can be managed surgically with complete cure. The aim of the report was to highlight BFH as a differential diagnosis of nasal mass in neonates and its excellent prognosis with excision with pathologically clear margins.
Conflicts of interest
All authors have none to declare.
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