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Primary Ewing sarcoma of the kidney: a case report and treatment review

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Abstract

Ewing sarcomas/primitive neuroectodermal tumors (ES/PNET) of the kidney are rarely found high-grade malignant tumors, offering poor prognosis. Although established treatment guidelines for ES of kidney are scarce, a multi-modality treatment approached is typically implemented. Herein, we report a 14-year-old female patient with ES of right kidney. Post-nephrectomy disease recurrence was treated with chemotherapy (i.e., vincristine, doxorubicin and cyclophosphamide); marked reduction in tumor size (i.e., from 18.5 × 11.3 cm2 to 3.7 × 2.2 cm2; ~96% reduction in size) as per computed tomography images was observed. We present our treatment experience and review from the available literature.

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Authors and Affiliations

  1. Center for Nuclear Medicine and Radiotherapy (CENAR), Quetta, Pakistan

    Muhammad Sadiq, Iftikhar Ahmad, Jamila Shuja & Khushnaseeb Ahmad

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  1. Muhammad Sadiq
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  2. Iftikhar Ahmad
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  3. Jamila Shuja
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  4. Khushnaseeb Ahmad
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Correspondence to Iftikhar Ahmad.

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It is declared that the results presented in this paper have not been published previously in whole or part. Furthermore, the authors have no conflict of interest.

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Sadiq, M., Ahmad, I., Shuja, J. et al. Primary Ewing sarcoma of the kidney: a case report and treatment review. CEN Case Rep 6, 132–135 (2017). https://doi.org/10.1007/s13730-017-0259-0

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  • DOI: https://doi.org/10.1007/s13730-017-0259-0

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