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Ossifying Fibroma: A Case Report of an Unusual Presentation of Angiodysplastic Disease with Review of Literature

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Abstract

Ossifying fibroma is a nonneoplastic developmental disease of osseous tissue seen rarely in association with Sturge–Weber syndrome. It is a lesion of unknown aetiology, uncertain pathogenesis, and diverse histopathology. The aim of this study is to report an unusual case of in a 11-year-old male of SWS. The rarity of the case and the fact that ossifying fibroma may be associated with Sturge–Weber syndrome propelled us to report it. Physical examination showed facial asymmetry (due to hemifacial swelling) without any tenderness, fluctuation, ocular pain, or ophthalmoplegia. Imaging studies revealed a solid mass involving the left maxilla and orbital floor. A conservative therapeutic approach to these lesions may be sufficient to relieve signs and symptoms effectively. Periodic follow-up is indicated to detect recurrences or malignant changes in the early stages.

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Authors and Affiliations

  1. Department of ENT, Armed Forces Medical College, Pune, 411040, India

    Sanjeeva Bharadwaja & Uma Patnaik

  2. Department of ENT, Command Hospital (Southern Command), Pune, 411040, India

    N. P. C. Rao & Abha Kumari

Authors
  1. Sanjeeva Bharadwaja
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  2. Uma Patnaik
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  3. N. P. C. Rao
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  4. Abha Kumari
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Correspondence to Sanjeeva Bharadwaja.

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Bharadwaja, S., Patnaik, U., Rao, N.P.C. et al. Ossifying Fibroma: A Case Report of an Unusual Presentation of Angiodysplastic Disease with Review of Literature. Indian J Otolaryngol Head Neck Surg 75, 1095–1104 (2023). https://doi.org/10.1007/s12070-022-03408-3

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  • DOI: https://doi.org/10.1007/s12070-022-03408-3

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