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Orthotropic heart transplantation for adult congenital heart disease: a case with heterotaxy and dextrocardia

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Abstract

A 41-year-old male with heterotaxy (left isomerism) and dextrocardia composed by single ventricle, absent inferior vena cava, bilateral superior vena cava (SVC), common atrioventricular valve has received orthotopic heart transplantation (HTx) after long waiting period as Status-1. Reconstructions of bilateral SVC and hepatic vein route were successful without use of prosthetic material, and the donor heart was placed in the left mediastinum. In spite of satisfactory early recovery, the patient expired 4 months after transplantation mainly from fungal infection which developed following humoral rejection. HTx for adult patients with complex congenital heart disease is demanding in technical as well as pre- and post-transplant management, and indication should be critically determined.

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Author notes

  1. Hajime Ichikawa

    Present address: National Cerebral and Cardiovascular Center, Osaka, Japan

Authors and Affiliations

  1. Department of Cardiovascular Surgery, Osaka University Graduate School of Medicine, Yamadaoka 2-2, Suita, Osaka, 565-0871, Japan

    Hikaru Matsuda, Norihide Fukushima, Hajime Ichikawa & Yoshiki Sawa

  2. Higashi Takarazuka Satoh Hospital, Nagaochou 2-1, Takarazuka, Hyogo, 665-0873, Japan

    Hikaru Matsuda

Authors
  1. Hikaru Matsuda
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  2. Norihide Fukushima
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  3. Hajime Ichikawa
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  4. Yoshiki Sawa
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Correspondence to Hikaru Matsuda.

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All the authors have declared no conflict of interest relating to this report.

Additional information

H. Matsuda: Professor Emeritus Osaka University.

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Matsuda, H., Fukushima, N., Ichikawa, H. et al. Orthotropic heart transplantation for adult congenital heart disease: a case with heterotaxy and dextrocardia. Gen Thorac Cardiovasc Surg 65, 47–51 (2017). https://doi.org/10.1007/s11748-015-0573-4

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  • DOI: https://doi.org/10.1007/s11748-015-0573-4

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