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Dental findings of hyperphosphatemic familial tumoral calcinosis

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Abstract

Tumoral calcinosis is a rare familial disorder characterized by masses of calcification in periarticular soft tissues. Few reports in the literature have described dental abnormalities in patients with tumoral calcinosis. These dental abnormalities include short bulbous roots, pulp stones, and obliteration of the pulp cavity. In this case report, we describe the dental radiographic findings in a patient with tumoral calcinosis; these findings were similar to dentin dysplasia. Periapical radiolucencies with noncarious teeth were observed in addition to the dental findings previously reported.

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Authors and Affiliations

  1. İzmir Dental Training Hospital, 35260, Konak, İzmir, Turkey

    Hümeyra Özge Yılancı

  2. Department of Dentomaxillofacial Radiology, Faculty of Dentistry, Hacettepe University, 06100, Sıhhiye, Ankara, Turkey

    Nursel Akkaya & Murat Özbek

  3. Department of Anatomy, Faculty of Medicine, Hacettepe University, 06100, Sıhhiye, Ankara, Turkey

    Hakan Hamdi Çelik & İlkan Tatar

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  1. Hümeyra Özge Yılancı
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  2. Nursel Akkaya
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  3. Murat Özbek
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  4. Hakan Hamdi Çelik
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  5. İlkan Tatar
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Correspondence to Hümeyra Özge Yılancı.

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Hümeyra Özge Yılancı, Nursel Akkaya, Murat Özbek, Hakan Hamdi Çelik, and İlkan Tatar declare that they have no conflict of interest.

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All procedures followed were in accordance with the ethical standards of the responsible committee on human experimentation (institutional and national) and with the Helsinki Declaration of 1964 and later versions. Informed consent was obtained from the patient for being included in the study.

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Yılancı, H.Ö., Akkaya, N., Özbek, M. et al. Dental findings of hyperphosphatemic familial tumoral calcinosis. Oral Radiol 33, 65–70 (2017). https://doi.org/10.1007/s11282-016-0237-9

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  • DOI: https://doi.org/10.1007/s11282-016-0237-9

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