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Magnetic resonance and computed tomography imaging of a grade IV papillary endolymphatic sac tumour

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Abstract

The endolymphatic sac tumour (ELST) is an adenomatous neoplasm of the papillary pattern originating from the endolymphatic sac’s epithelium. We describe the computed tomography and magnetic resonance imaging features of a rare grade IV tumour with extensive skull base, cerebello-pontine and nasopharyngeal spread as well as involvement of the left temporomandibular joint. Papillary ELST may easily be misinterpreted on histopathological and even on immunohistochemical examination with other papillary lesions. Thus the radiological imaging features and localization in conjunction with histopathological features and clinical presentation play a paramount role in making the correct diagnosis.

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Acknowledgements

We wish to acknowledge Professor James W Loock, Department of Otorhinolaryngology and Professors Savvas Andronikou and Jan W Lotz, Department of Diagnostic Radiology for their suggestions.

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Authors and Affiliations

  1. Department of Diagnostic Radiology, Tygerberg Academic Hospital, Faculty of Health Sciences, University of Stellenbosch, Cape Town, Republic of South Africa

    Pieter Janse van Rensburg

  2. Suite 92, Private Bag X22, Tygervallei, 7536, Republic of South Africa

    Pieter Janse van Rensburg

  3. Department of Otorhinolaryngology, Tygerberg Academic Hospital, Faculty of Health Sciences, University of Stellenbosch, Cape Town, Republic of South Africa

    Graeme van der Meer

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  1. Pieter Janse van Rensburg
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  2. Graeme van der Meer
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Correspondence to Pieter Janse van Rensburg.

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Janse van Rensburg, P., van der Meer, G. Magnetic resonance and computed tomography imaging of a grade IV papillary endolymphatic sac tumour. J Neurooncol 89, 199–203 (2008). https://doi.org/10.1007/s11060-008-9605-6

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  • DOI: https://doi.org/10.1007/s11060-008-9605-6

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