Abstract
We describe the first known case of congenital lymphoedema associated with selective deficit of naïve CD4+ T-lymphocytes. A high proportion of naïve CD4+ T-lymphocytes was found in the ascitic fluid, supporting the hypothesis of extra-vascular sequestration of these cells into lymphoedematous tissue.
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Abbreviations
- ICL :
-
idiopathic CD4+ lymphocytopenia
References
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Chiappini, E., Galli, L., Giudizi, M.G. et al. Selective deficiency of naïve CD4+ T-lymphocytes in a child with congenital lymphoedema. Eur J Pediatr 162, 752–754 (2003). https://doi.org/10.1007/s00431-003-1295-7
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DOI: https://doi.org/10.1007/s00431-003-1295-7