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Cochlear implantation in patients with Cogan syndrome: long-term results

  • Otology
  • Published:
European Archives of Oto-Rhino-Laryngology Aims and scope Submit manuscript

Abstract

The objective of this study was to evaluate the long-term outcomes of patients with Cogan syndrome (CS) who have undergone cochlear implantation. Subjects consisted of 12 cochlear implant users with a typical form of CS. Measures included word and sentence recognition scores. The speech recognition performance was rated before cochlear implantation and at 1 and 5 years after implantation. The speech materials were presented in quiet only condition. The mean 12-month post-operative word and sentence recognition scores were 91.4 and 93.1 %, respectively. Five years after implantation, the group means for word and sentence recognition tests were 94 and 96.3 %, respectively. No patients in this series experienced flap complication or other local or systemic complications. This long-term study on 12 subjects with CS over 5 years of cochlear implant use reveals that cochlear implantation is safe in the long term and provides excellent and stable hearing results.

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Authors and Affiliations

  1. Department of Clinical and Experimental Medicine, Unit of Audiology and Pediatric Otorhinolaryngology, University-Hospital of Parma, Via Gramsci 14, 43123, Parma, Italy

    Andrea Bacciu, Enrico Pasanisi, Filippo Di Lella, Maurizio Guida, Salvatore Bacciu & Vincenzo Vincenti

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  1. Andrea Bacciu
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  2. Enrico Pasanisi
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  3. Filippo Di Lella
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  4. Maurizio Guida
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  5. Salvatore Bacciu
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  6. Vincenzo Vincenti
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Correspondence to Andrea Bacciu.

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Bacciu, A., Pasanisi, E., Di Lella, F. et al. Cochlear implantation in patients with Cogan syndrome: long-term results. Eur Arch Otorhinolaryngol 272, 3201–3207 (2015). https://doi.org/10.1007/s00405-014-3376-9

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  • DOI: https://doi.org/10.1007/s00405-014-3376-9

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