Abstract
This report presents the case of a 6-day-old male with cystic biliary atresia (CBA), and the cyst was detected antenatally. Antenatal ultrasonography suggested the possibility of CBA or a choledochal cyst at 16 weeks’ gestation. However, the cyst disappeared during the later gestational period. The cyst was detected again by preoperative imaging. Surgical cholangiography at 30 days of age confirmed CBA, but the common hepatic duct (CHD) was extremely narrow. The histopathological findings revealed the partial obstruction of CHD. These findings suggest that correctable CBA (I cyst) may change into uncorrectable CBA (IIId).
References
Casaccia G, Bilancioni E, Nahom A, Trucchi A, Aite L, Marcellini M, Bagolan P (2002) Cystic anomalies of biliary tree in the fetus: is it possible to make a more specific prenatal diagnosis? J Pediatr Surg 37:1191–1194
Matsubara H, Oya N, Suzuki Y, Kajiura S, Suzumori K, Matsuo Y, Suzuki T, Hashimoto T (1997) Is it possible to differentiate between choledochal cyst and congenital biliary atresia (type I cyst) by antenatal ultrasonography? Fetal Diagn Ther 12:306–308
Redkar RR, Davenport M, Howard ER (1998) Antenatal diagnosis of congenital anomalies of the biliary tract. J Pediatr Surg 33:700–704
Hinds R, Davenport M, Mieli-Vergani G, Hadzic N (2004) Antenatal presentation of biliary atresia. J Pediatr 144:43–46
Saito T, Horie H, Yoshida H, Matsunaga T, Kouchi K, Kuroda H, Etoh T, Higashimoto Y, Kuriyama H, Ohnuma N (2006) The perinatal transition of the hepatobiliary cyst size provides information about the condition of bile flow in biliary cystic malformation cases. J Pediatr Surg 41:1397–1402
Caponcelli E, Knisely AS, Davenport M (2008) Cystic biliary atresia: an etiologic and prognostic subgroup. J Pediatr Surg 43:1619–1624
Fujishiro J, Iwanaka T, Arai M, Kawashima H, Kudou S, Imaizumi S, Hirukawa S, Inasaka O (2005) Disappearing cyst of the hepatic hilum in uncorrectable biliary atresia. Pediatr Surg Int 21:116–118
Nakada M, Nakada K, Kitagawa H, Wakisaka M, Den M (2000) Biliary atresia with cystic dilatation of the bile duct detected antenatally—report of a case showing dense connective tissue mass at the Porta Hepatis. J Jpn Soc Pediatr Surg 36:332–337
Kawasaki M, Nakata S, Takao T (2009) A case of congenital biliary atresia observed from prenatal period. J Jpn Soc Pediatr Surg 45:729–732
Nio M, Sano N, Ishii T, Sasaki H, Hayashi Y, Ohi R (2006) Long-term outcome in type I biliary atresia. J Pediatr Surg 41:1973–1975
Hasegawa T, Sasaki T, Kimura T, Sawai T, Nose K, Kamata S, Okada A, Wada K, Kanzaki T (2002) Prenatal ultrasonographic appearance of type IIId (uncorrectable type with cystic dilatation) biliary atresia. Pediatr Surg Int 18:425–428
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The authors would like to thank Mr. Brian Quinn for reviewing the English used in this manuscript.
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Masumoto, K., Kai, H., Oka, Y. et al. A case of cystic biliary atresia with an antenatally detected cyst: the possibility of changing from a correctable type with a cystic lesion (I cyst) to an uncorrectable one (IIId). Pediatr Surg Int 27, 99–102 (2011). https://doi.org/10.1007/s00383-010-2715-1
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DOI: https://doi.org/10.1007/s00383-010-2715-1