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Biliary atresia with associated complicated anorectal and urogenital malformations

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Abstract

We report on a girl with biliary atresia (BA) who also suffered with anorectal agenesis without fistula and complicated urogenital malformation. The outcome of patients with these severe anomalies is poor, but she has survived without liver and/or renal transplantation for more than 3 years. A careful treatment plan for each anomaly in addition to prevention of cholangitis and urinary tract infection is indispensable for managing these complicated anomalies.

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Authors and Affiliations

  1. Department of Pediatric Surgery, Graduate School of Medicine, Tohoku University, 1-1 Seiryo-machi, 980-8574, Sendai , Aoba-ku, Japan

    Shintaro Amae, Takamichi Kamiyama, Masaki Nio, Shigehiko Yoshida & Ryoji Ohi

  2. Department of Pediatric Surgical Oncology, Graduate School of Medicine, Tohoku University, Sendai, Japan

    Yutaka Hayashi

  3. Department of Pediatric Urology, Kobe Children’s Hospital, Kobe, Japan

    Saburo Tanikaze

Authors
  1. Shintaro Amae
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  2. Takamichi Kamiyama
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  3. Masaki Nio
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  4. Shigehiko Yoshida
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  5. Yutaka Hayashi
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  6. Saburo Tanikaze
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  7. Ryoji Ohi
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Correspondence to Ryoji Ohi.

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Amae, S., Kamiyama, T., Nio, M. et al. Biliary atresia with associated complicated anorectal and urogenital malformations. Ped Surgery Int 20, 380–383 (2004). https://doi.org/10.1007/s00383-004-1203-x

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  • DOI: https://doi.org/10.1007/s00383-004-1203-x

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