Abstract
Epidermoid cysts are composed of stratified squamous epithelium, which develop from inclusion of ectodermal tissue remnants entrapped during primitive neural tube closure period between the 3rd and 5th weeks of gestation. Intramedullary epidermoid cysts (IEC) are very rare in childhood. Eleven cases have been reported previously. Even though it is a rare entity, early diagnosis with timely fashioned surgical treatment has a great influence on patients’ symptoms, especially if there are myelopathic findings. In this case report, we demonstrate this fact with a demonstrative clinical case and review radiological, pathological, and surgical perspectives with literature review.
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Gonzalvo A, Hall N, McMahon JH, Fabinyi GC (2009) Intramedullary spinal epidermoid cyst of the upper thoracic region. J Clin Neurosci Off J Neurosurg Soc Austral 16(1):142–144. doi:10.1016/j.jocn.2008.04.017
Fereydoonian NA, Bakhti S, Fereshtehnejad SM, Tabibkhooei AR (2013) Intramedullary thoracic spine epidermoid cyst with myelopathic presentations: a report of a rare case. Clin Neurol Neurosurg 115(6):841–843. doi:10.1016/j.clineuro.2012.08.002
Cataltepe O, Berker M, Akalan N (2004) A giant intramedullary spinal epidermoid cyst of the cervicothoracic region. Pediatr Neurosurg 40(3):120–123. doi:10.1159/000079853
Hullay J, Oszlanszky O, Halasz P (1962) Intramedullar epidermoid successfully operated upon. Acta Neurochir 10:410–414
Tekkok IH, Palaoglu S, Erbengi A, Onol B (1992) Intramedullary epidermoid cyst of the cervical spinal cord associated with an extraspinal neuroenteric cyst: case report. Neurosurgery 31(1):121–125
Roux A, Mercier C, Larbrisseau A, Dube LJ, Dupuis C, Del Carpio R (1992) Intramedullary epidermoid cysts of the spinal cord. Case report. J Neurosurg 76(3):528–533. doi:10.3171/jns.1992.76.3.0528
Onder A, Kadioglu H, Takci E, Kayaoglu C, Tuzun Y, Gundogdu C, Aydin IH (1993) Intramedullary epidermoid Cyst (a case report). Turk Norosirurji Dergisi 3:41–44
Jadhav RN, Khan GM, Palande DA (1999) Intramedullary epidermoid cyst in cervicodorsal spinal cord. J Neurosurg 90(1 Suppl):161
Rocha Junior MA, de Carvalho GT, Faria MP, Faglioni W Jr, de Souza AA (2003) Intramedullary epidermoid tumor: case report. Arq Neuropsiquiatr 61(3B):867–869
Ferrara P, Costa S, Rigante D, Mule A, D’Aleo C, Pulitano S, Belli P, Menchinelli P, Caldarelli M (2003) Intramedullary epidermoid cyst presenting with abnormal urological manifestations. Spinal Cord 41(11):645–648. doi:10.1038/sj.sc.3101482
Kumar R, Singh V (2004) Intramedullary mass lesion of the spinal cord in children of a developing milieu. Pediatr Neurosurg 40(1):16–22. doi:10.1159/000076572
Kumar A, Singh P, Jain P, Badole CM (2010) Intramedullary spinal epidermoid cyst of the cervicodorsal region: a rare entity. J Pediatr Neurosci 5(1):49–51. doi:10.4103/1817-1745.66675
Zavanone M, Guerra P, Rampini PM, Crotti F, Vaccari U (1991) A cervico-dorsal intramedullary epidermoid cyst. Case report and review of the literature. J Neurosurg Sci 35(2):111–115
Brohi SR, Qureshi SM, Rajput SS, Bhatti NK (2010) Thoracic intramedullary epidermoid with paraplegia for 12 years. Journal of the College of Physicians and Surgeons--Pakistan : JCPSP 20 (2):135-136. doi:02.2010/JCPSP.135136
Fazio MG, Kil AM, Rooks VJ, Biega TJ (2013) Diffusion-weighted magnetic resonance imaging of an intramedullary epidermoid cyst with dorsal dermal sinus tract in a toddler. Case Rep Radiol 2013:878713. doi:10.1155/2013/878713
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Murat Şakir Ekşi, M.D. was supported by a grant from Tubitak (The Scientific and Technological Research Council of Turkey), Grant Number 1059B191400255).
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Babayev, R., Abbasov, B. & Ekşi, M.Ş. Thoracic intramedullary epidermoid cyst-timely fashion diagnosis and treatment. Childs Nerv Syst 31, 793–796 (2015). https://doi.org/10.1007/s00381-015-2625-6
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DOI: https://doi.org/10.1007/s00381-015-2625-6