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Scimitar syndrome: morphological diagnosis and assessment of hemodynamic significance by magnetic resonance imaging

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Abstract

Scimitar syndrome has a variable presentation depending on the age at which the diagnosis is made. We report a case of a young woman (age 18 years) with suspected right pulmonary hypoplasia in whom a scimitar syndrome was diagnosed. Using MRI morphological findings and hemodynamic significance of the syndrome were assessed. Left-to-right shunt was calculated from blood flow measurements performed in the ascending aorta, the main pulmonary artery, and the aberrant scimitar vein.

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Authors and Affiliations

  1. Department of Diagnostic Radiology, University of Tuebingen, Hoppe-Seyler-Strasse 3, 72076, Tuebingen, Germany

    Ulrich Kramer, Volker Dörnberger, Michael Fenchel, Norbert Stauder, Claus D. Claussen & Stephan Miller

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  1. Ulrich Kramer
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  2. Volker Dörnberger
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  3. Michael Fenchel
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  4. Norbert Stauder
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  5. Claus D. Claussen
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  6. Stephan Miller
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Correspondence to Ulrich Kramer.

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Kramer, U., Dörnberger, V., Fenchel, M. et al. Scimitar syndrome: morphological diagnosis and assessment of hemodynamic significance by magnetic resonance imaging. Eur Radiol 13 (Suppl 6), L147–L150 (2003). https://doi.org/10.1007/s00330-003-2061-y

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  • DOI: https://doi.org/10.1007/s00330-003-2061-y

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