Skip to main content

Advertisement

Log in

The sagging rope sign in achondroplasia—different from Perthes’ disease

  • Scientific Article
  • Published:
Skeletal Radiology Aims and scope Submit manuscript

Abstract

Objective

The sagging rope sign is a radio-opaque line, seen on radiographs of the hips, with Perthes’ disease. The main purpose of this study was to determine the incidence, cause and importance of this sign in achondroplasia, and to reveal how it differs from in Perthes’ disease.

Design

Serial radiograms, along with 2-dimensional and 3-dimensional CT images were studied in 42 achondroplasic patients.

Patients

Forty-two achondroplasic patients, reported at our institute (for routine outpatient consultation, spine surgeries, deformity corrections, limb-lengthening procedures) were included in this study. There were 26 males and 16 females.

Results

The sign was observed bilaterally, in all patients. Evaluation of CT images revealed spherical heads, with presence of circumferential overhang in all hips. This circumferential overhang, seen on 3-D CT scan, corresponded to the sagging rope sign on radiographs.

Conclusions

Presence of the sagging rope sign in bilateral hips is a characteristic feature of achondroplasia. It usually appears before epiphyseal closure. Its cause, incidence, and nature differ from Perthes’ disease, and its presence does not carry a bad prognosis in achondroplasia.

This is a preview of subscription content, log in via an institution to check access.

Access this article

Price excludes VAT (USA)
Tax calculation will be finalised during checkout.

Instant access to the full article PDF.

Institutional subscriptions

Fig. 1
Fig. 2
Fig. 3
Fig. 4
Fig. 5
Fig. 6
Fig. 7
Fig. 8

Similar content being viewed by others

References

  1. Apley AG, Wientroub S. The sagging rope sign in Perthes disease and allied disorders. J Bone Joint Surg Br 1981;63(1):43–47

    PubMed  Google Scholar 

  2. Clarke NM, Harrison MH, Keret D. The sagging rope sign: a critical appraisal. J Bone Joint Surg Br 1983;65(3):285–287

    PubMed  CAS  Google Scholar 

  3. Kim HT, Eisenhauer E, Wenger DR. The “sagging rope sign” in avascular necrosis in children’s hip diseases –confirmation by 3D CT studies. Iowa Orthop J 1995;15:101–111

    PubMed  CAS  Google Scholar 

  4. Kim HT, Wenger DR. “Functional retroversion” of the femoral head in Legg–Calve–Perthes disease and epiphyseal dysplasia: analysis of head-neck deformity and its effect on limb position using three-dimensional computed tomography. J Pediatr Orthop 1997;17(2):240–246

    Article  PubMed  CAS  Google Scholar 

  5. Herring JA. Skeletal dysplasias: achondroplasia. Tachdjian’s pediatric orthopaedics, vol. 3, 3rd ed. Philadelphia: W. B. Saunders Company; 2002. p 1510–1521

    Google Scholar 

  6. Ponseti IV. Skeletal growth in achondroplasia. J Bone Joint Surg Am 1970;52(4):701–716

    PubMed  CAS  Google Scholar 

  7. Maynard JA, Ippolito EG, Ponseti IV, et al. Histochemistry and ultrastructure of the growth plate in achondroplasia. J Bone Joint Surg Am 1981;63(6):969–979

    PubMed  CAS  Google Scholar 

  8. Bailey JA. Orthopaedic aspects of achondroplasia. J Bone Joint Surg Am 1970;52(7):1285–1301

    PubMed  Google Scholar 

  9. Stulberg SD, Cooperman DR, Wallensten R. The natural history of Legg–Calve–Perthes’ disease. J Bone Joint Surg Am 1981;63:1095–1108

    PubMed  CAS  Google Scholar 

Download references

Author information

Authors and Affiliations

Authors

Corresponding author

Correspondence to Viraj Uttamrao Shingade.

Additional information

Study conducted at: Department of Paediatric Orthopaedics, Korea University, Guro Hospital, #80, Guro-Gu, Guro-dong, Seoul, Korea

Rights and permissions

Reprints and permissions

About this article

Cite this article

Shingade, V.U., Song, HR., Lee, SH. et al. The sagging rope sign in achondroplasia—different from Perthes’ disease. Skeletal Radiol 35, 923–928 (2006). https://doi.org/10.1007/s00256-006-0166-5

Download citation

  • Received:

  • Accepted:

  • Published:

  • Issue Date:

  • DOI: https://doi.org/10.1007/s00256-006-0166-5

Keywords

Navigation