Abstract
We describe a 2-month-old female infant with a univentricular heart and overly tightened pulmonary artery band (PAB) resulting in hypercyanotic episodes. Despite adequate doses of morphine and a beta-blocker, she continued to have multiple hypercyanotic events per day. Treatment with fludrocortisone resulted in resolution of these episodes and allowed performance of a Glenn shunt at 3 half months of age. We conclude that fludrocortisone may be beneficial in the management of an overly tightened PAB until the patient is suitable for surgical intervention.
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Balaji S, Oslizlok PC, Alien MC, McKay CA, Gillette PC (1994) Neurocardiogenie syncope in children with a normal heart. J Am Coll Cardiol 23:779–785
Jureidini SB, Alpert BS, Durant RH, Reyes LK, Nouri S (1986) Two-dimensional echocardiographic assessment of adequacy of pulmonary artery banding. Pediatr Cardiol 6:239–244
Massin MM (2003) Neurocardiogenic syncope in children: current concepts in diagnosis and treatment. Pediatr Drugs 5:327–334
Nicolas RT, Hills C, Moller JH, Huddleston CB, Johnson MC (2005) Early outcome after Glenn shunt and Fontan palliation and the impact of operation during viral respiratory season: analysis of a 19-year multi-institutional experience. Ann Thorac Surg 79:613–6l7
Rudolph AM, Danilowicz D (1963) Treatment of severe spell syndrome in congenital heart disease. Pediatrics 32:141–143
Scott WA, Pongiglione G, Bromberg BI, et al. (1995) Randomized comparison of atenolol and fludrocortisone acetate in the treatment of pediatric neurally mediated syncope. Am J Cardiol 76:400–402
Simpson IA, Valdez-Cruz LM, Berthoty DP, et al. (1993) Cine magnetic resonance imaging and color Doppler flow mapping in infants and children with pulmonary artery bands. Am J Cardiol 71:1419–1426
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Ponciroli, K., Jureidini, S., Dempsher, D. et al. Fludrocortisone in the Management of an Infant with a Single Ventricle and an Overly Tightened Pulmonary Artery Band. Pediatr Cardiol 27, 640–642 (2006). https://doi.org/10.1007/s00246-005-1120-3
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DOI: https://doi.org/10.1007/s00246-005-1120-3