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Alveoläres Weichteilsarkom

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Zusammenfassung

Das alveoläre Weichteilsarkom ist ein bösartiger Tumor, dessen Entstehungsursache noch nicht geklärt ist. Die mikrohistopathologischen Untersuchungen zeigen ein alveoläres oder pseudoglanduläres Bild. Gleichzeitig sind PAS-positive, diastaseresistente intrazytoplasmatische Einschlüsse für diesen Tumor charakteristisch. Dieser Tumor befällt im Bereich von Kopf und Hals überwiegend die Zunge und Teile der Orbita.

Die primäre Therapie dieses Tumors ist die totale Entfernung, die dann mit Radiotherapie oder Chemotherapie kombiniert werden kann.

In der vorliegenden Studie handelt es sich um eine 17-jährige Patientin. Wir haben den Tumor total entfernt und anschließend mit Radiotherapie behandelt. Die postoperativen Untersuchungen über 3 Jahre ergaben keinerlei lokalen Herd oder Fernmetastasen.

Abstract

Alveolar soft part sarcoma is a malignant soft part tumor the etiology of which has not yet been clarified. Histopathological examinations show an alveolar or pseudoglandular pattern. PAS-positive, diastase resistant intraplasmic inclusion bodies are characteristic for this tumor which occurs in the head and neck region; mainly the tongue and the orbita. Primary therapy includes total resection which can later be combined with radiotherapy or chemotherapy. The present study involves a 17 year old patient. We totally removed the tumor and then used radiotherapy. The postoperative examinations over 3 years showed neither local recurrence nor distant metastases.

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Authors and Affiliations

  1. Hals-Nasen-Ohren-Klinik der Medizinischen Fakultät Cerrahpasa, İstanbul, Türkei

    E. İnci, N. Korkut, M. Erem & N. Kalekoğlu

  2. İ.Ü. Cerrahpaşa Tip Fakültesi, KBB Anabilim Dali, Fatih/İstanbul, Türkei

    E. İnci

Authors
  1. E. İnci
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  2. N. Korkut
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  3. M. Erem
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  4. N. Kalekoğlu
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Correspondence to E. İnci.

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İnci, E., Korkut, N., Erem, M. et al. Alveoläres Weichteilsarkom. HNO 52, 145–149 (2004). https://doi.org/10.1007/s00106-003-0872-4

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