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Pulmonary lymphangioleiomyoma in a patient with multiple endocrine neoplasia Type I

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Abstract

The multiple endocrine neoplasia (M.E.N.) syndromes consist of a group of proliferative disorders that selectively target specific sets of endocrine and soft tissue cells. Here we report a case of lymphangioleiomyoma of the lung in a patient with multiple endocrine neoplasia Type I (M.E.N. I). This is the first time such an association has been reported. In our opinion it could possibly be ascribed to the genetic predisposition to proliferative disorders of patients with M.E.N. syndromes.

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Authors and Affiliations

  1. Cattedra di Medicina Interna 4, Istituto di II Clinica Medica, Università degli Studi di Roma “La Sapienza”, Roma, Italy

    V. Carnevale, E. Romagnoli, E. D’Erasmo, G. Spagna, R. Rosso, S. Minisola M.D. & G. F. Mazzuoli

  2. Servizio di Anatomia ed Istologia Patologica e Citologia Diagnostica, Azienda Ospedaliera Complesso Ospedaliero San Giovanni Addolorata, Roma, Italy

    D. Remotti

Authors
  1. V. Carnevale
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  2. E. Romagnoli
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  3. D. Remotti
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  4. E. D’Erasmo
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  5. G. Spagna
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  6. D. Pisani
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  7. R. Rosso
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  8. S. Minisola M.D.
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  9. G. F. Mazzuoli
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Carnevale, V., Romagnoli, E., Remotti, D. et al. Pulmonary lymphangioleiomyoma in a patient with multiple endocrine neoplasia Type I. J Endocrinol Invest 20, 282–285 (1997). https://doi.org/10.1007/BF03350301

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  • DOI: https://doi.org/10.1007/BF03350301

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