Abstract
Five patients between 3 to 54 months of age presented with normocytic anemia with erythroblastopenia. All of them had normal milestones without any developmental delay or physical anomalies. Inheritance appeared to be autosomal recessive in one case. Of the four patients treated, two responded to corticosteroids, of which one developed late resistance. One patient responded to oxymetholone and the other was refractory to both cortico-steroids and androgen therapy.
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Agarwal, R.K., Moudgil, A., Pati, H. et al. Congenital pure red cell aplasia in northern India. Indian J Pediatr 52, 97–102 (1985). https://doi.org/10.1007/BF02754728
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DOI: https://doi.org/10.1007/BF02754728