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Laryngeal involvement in pediatric neurofibromatosis: a case report and review of the literature

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Abstract

A case of neurofibroma of the larynx occurring in generalized neurofibromatosis (von Recklinghausen's disease) is presented, and the previously reported pediatric cases are reviewed. Laryngeal involvement in neurofibromatosis is rare and the predominant signs and symptoms include dyspnea, stridor, loss or change of voice and dysphagia. Problems posed related to diagnosis, management and course of this infrequent laryngeal localization are discussed.

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Masip, M.J., Esteban, E., Alberto, C. et al. Laryngeal involvement in pediatric neurofibromatosis: a case report and review of the literature. Pediatr Radiol 26, 488–492 (1996). https://doi.org/10.1007/BF01377206

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  • DOI: https://doi.org/10.1007/BF01377206

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