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Intestinal carcinoid tumor and myotonic dystrophy

A new association?

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Summary

The occurrence of multiple carcinoid tumors of the small bowel with liver metastases is reported in a patient with a previous myotonic dystrophy. In addition to the association of myotonic dystrophy with multiple endocrine adenomatosis type 2A, hyperparathyroidism, and neurofibromatosis, this case report gives further evidence for the propensity of such patients to develop neuroendocrine tumors.

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Authors and Affiliations

  1. Service d'Hépato-Gastroentérologie et d'Assistance Nutritive, Hôpital de Hautepierre, Avenue Molière, 67098, Strasbourg, Cedex, France

    J. M. Reimund MD, B. Duclos MD, P. Chamouard MD, J. M. Warter MD, PhD, J. P. Weill MD, PhD & R. Baumann MD, PhD

  2. Service de Neurologie, Hôpital Central, 67085, Strasbourg, France

    J. M. Reimund MD, B. Duclos MD, P. Chamouard MD, J. M. Warter MD, PhD, J. P. Weill MD, PhD & R. Baumann MD, PhD

Authors
  1. J. M. Reimund MD
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  2. B. Duclos MD
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  3. P. Chamouard MD
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  4. J. M. Warter MD, PhD
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  5. J. P. Weill MD, PhD
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  6. R. Baumann MD, PhD
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Reimund, J.M., Duclos, B., Chamouard, P. et al. Intestinal carcinoid tumor and myotonic dystrophy. Digest Dis Sci 37, 1922–1925 (1992). https://doi.org/10.1007/BF01308090

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  • DOI: https://doi.org/10.1007/BF01308090

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