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Dystone Bewegungsstörungen bei Kindern

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Pädiatrische Neurochirurgie

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Zusammenfassung

Bei den Dystonien handelt es sich um eine heterogene Gruppe verschiedenartiger Erkrankungen mit ähnlichen Symptomen. Klassifikation, Differenzialdiagnosen und Therapien sind komplex und sollten von spezialisierten Zentren durchgeführt werden. Die Erkrankungen können vom Säuglings- bis ins späte Erwachsenenalter auftreten. Das Spektrum reicht von oligosymptomatischen Formen bis hin zu solchen, die schwerste Beeinträchtigungen in der Lebensqualität und Behinderungen bedingen können. Zur konservativen Therapie werden Krankengymnastik, orale Medikamente sowie lokale Injektionsbehandlungen eingesetzt. Von neurochirurgisch operativer Seite existieren die Neuromodulationstherapien (implantierbare Pumpen, Tiefe Hirnstimulation) sowie ablative Verfahren. Die neuere Literatur zeigt, dass insbesondere die kognitive Entwicklung bei Kindern umso günstiger beeinflusst werden kann, je früher eine effektive Therapie erfolgt.

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Authors and Affiliations

  1. Neurochirurgie, Centre Hospitalier de Luxembourg, 4, rue Ernest Barblé, Europa, 1210, Luxembourg

    F. Hertel

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  1. F. Hertel
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Correspondence to F. Hertel .

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Editors and Affiliations

  1. Sektionsleiterin Pädiatrische Neurochirurgie, Neurochirurgische Klinik Universitätsklinikum, Heidelberg, Germany

    Heidi Bächli

  2. Universitätskinderklinik beider Basel (UKBB), Binningen, Switzerland

    Jürg Lütschg

  3. Chefärztin der Abteilung Kinderneurochirurgie Asklepios Kinderklinik, Sankt Augustin, Germany

    Martina Messing-Jünger

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Hertel, F. (2018). Dystone Bewegungsstörungen bei Kindern. In: Bächli, H., Lütschg, J., Messing-Jünger, M. (eds) Pädiatrische Neurochirurgie. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-48700-6_52

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  • DOI: https://doi.org/10.1007/978-3-662-48700-6_52

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  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-662-48699-3

  • Online ISBN: 978-3-662-48700-6

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