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Practical Pediatric Dermatology pp 51–59Cite as

Childhood Pityriasis Rubra Pilaris

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Abstract

Pityriasis rubra pilaris (PRP), characterized by the appearance of follicular hyperkeratotic papules, erythematosquamous plaques, and palmoplantar keratoderma, is an uncommon disorder of cornification in children. Most cases of PRP are sporadic and acquired, but a familial type with an autosomal mode of inheritance has been recognized in children. There is bimodal age distribution of the disease onset in children, with almost equal sex distribution. PRP is an uncommon disease with prevalence varying from 1 in 5000 to 1 in 50,000 in different populations, but incidence as high as about 1 case in every 500 new pediatric dermatology patients has been reported.

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Authors and Affiliations

  1. Dermatology Unit, Department of Medicine, Faculty of Medicine, Kuwait University, Kuwait, Kuwait

    Nawaf Al-Mutairi MD

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  1. Nawaf Al-Mutairi MD
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Correspondence to Nawaf Al-Mutairi MD .

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Editors and Affiliations

  1. Rotterdam, The Netherlands

    Arnold P. Oranje

  2. Farwaniya, Kuwait

    Nawaf Al-Mutairi

  3. Department of Dermatology, Henry Ford Hospital, Detroit, Michigan, USA

    Tor Shwayder

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Al-Mutairi, N. (2016). Childhood Pityriasis Rubra Pilaris. In: Oranje, A., Al-Mutairi, N., Shwayder, T. (eds) Practical Pediatric Dermatology. Springer, Cham. https://doi.org/10.1007/978-3-319-32159-2_6

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  • DOI: https://doi.org/10.1007/978-3-319-32159-2_6

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-32157-8

  • Online ISBN: 978-3-319-32159-2

  • eBook Packages: MedicineMedicine (R0)

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