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Retinal Pigment Epithelial Tumors

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Clinical Ophthalmic Oncology

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Abstract

Tumors of the retinal pigment epithelium (RPE) can be congenital or acquired. In this chapter, we review the clinical features of congenital and acquired tumors of the RPE and their possible systemic associations. In fact, those present at birth can be associated with systemic conditions such as familial adenomatous polyposis (FAP) or neurofibromatosis 2 (NF2). While most congenital tumors have quite characteristic clinical features that allow their accurate diagnosis, acquired RPE tumors are sometimes difficult to differentiate from choroidal neoplasms; therefore, it’s important to know the characteristics that RPE tumors show at the multimodal imaging.

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Authors and Affiliations

  1. Department of Ophthalmology, City of Health and Science Hospital, Turin, Italy

    Matteo Scaramuzzi

  2. Department of Pediatric Ophthalmology, Cole Eye Institute, Cleveland Clinic, Cleveland, OH, USA

    Elias I. Traboulsi

  3. Cole Eye Institute, Cleveland Clinic, Cleveland, OH, USA

    Arun D. Singh

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  1. Matteo Scaramuzzi
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  2. Elias I. Traboulsi
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  3. Arun D. Singh
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Correspondence to Elias I. Traboulsi .

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Editors and Affiliations

  1. Cleveland Clinic Foundation, Cole Eye Institute, Cleveland Clinic Foundation, Cleveland, OH, USA

    Arun D. Singh

  2. Moorfields Eye Hospital, City Rd, London, UK

    Bertil E. Damato

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Scaramuzzi, M., Traboulsi, E.I., Singh, A.D. (2024). Retinal Pigment Epithelial Tumors. In: Singh, A.D., Damato, B.E. (eds) Clinical Ophthalmic Oncology. Springer, Cham. https://doi.org/10.1007/978-3-031-72433-6_6

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