Abstract
Frontotemporal dementia (FTD) is a clinical term that encompasses a spectrum of disorders that affect predominantly language and behavior to varying degrees. Progressive nonfluent aphasia (PNFA) affects mainly language output, semantic dementia (SD) affects mainly language comprehension, and behavioral variant FTD (bv-FTD) affects mainly behavior. FTD is the most common form of young onset dementia. In this chapter, the main clinical, neuropsychological, radiological, and biomarker characteristics are described. Treatment is largely symptomatic but progress in the pathological, molecular, and genetic classification of FTD continues to burgeon, leading to exciting possibilities for disease modification.
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© 2011 Springer-Verlag London Limited
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Doherty, C.P., Hutchinson, S., Abrahams, S., Coen, R.F. (2011). Frontotemporal Dementia. In: Hardiman, O., Doherty, C. (eds) Neurodegenerative Disorders. Springer, London. https://doi.org/10.1007/978-1-84996-011-3_6
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DOI: https://doi.org/10.1007/978-1-84996-011-3_6
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